Tetralogy of Fallot with Unilateral Pulmonary Atresia

Abstract

Four patients with tetralogy of Fallot syndrome, whose physical and x-ray findings were distinctly unusual, are presented in this report. All these patients were demonstrated to have functional or anatomic atresia of one of the main pulmonary arteries, in addition to the characteristic features of the tetralogy of Fallot. Diagnostic criteria, including angiocardiograms, are presented, and the therapeutic implications are discussed.