Splenic Scintigraphy and Radionuclide Venography in the Heterotaxy Syndrome

Abstract

The heterotaxy syndrome may include complex congenital cardiovascular disease, visceral heterotaxia, bronchopulmonary abnormalities, and asplenia or polysplenia. These patients readily lend themselves to radionuclide venography and hepatic and splenic camera studies. In examination of ten patients, the authors found 99Tc sulfur colloid a useful tool in the diagnosis of polysplenia, asplenia, varying degrees of abdominal heterotaxia, and inferior vena cava abnormalities, including absence of its renal-to-hepatic portion, left-sided inferior vena cava, and double inferior vena cava.