Concepedia

Glycogen Storage Disease Type 1: Impact of Medium-Chain Triglycerides on Metabolic Control and Growth

Anibh M. Das, Thomas Lücke, Uta Meyer, Hans Hartmann, Sabine Illsinger

Annals of Nutrition and Metabolism · 2010 · 47 citations · 6 references

DOI

Abstract

MCT supplementation had a positive effect on metabolic control and growth in our patients suffering from GSD 1.

References

6

Glycogen storage disease type I: diagnosis, management, clinical course and outcome. Results of the European Study on Glycogen Storage Disease Type I (ESGSD I)

Jan Peter Rake, Gepke Visser, Philippe Labrune et al. · European Journal of Pediatrics · 2002 · 320 citations

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Malonyl coenzyme A and the regulation of functional carnitine palmitoyltransferase-1 activity and fat oxidation in human skeletal muscle

Blake B. Rasmussen, Ulf Holmbäck, Elena Volpi et al. · Journal of Clinical Investigation · 2002 · 188 citations · Full text

Age- and sex-specific pediatric reference intervals for biochemistry analytes as measured with the Ektachem-700 analyzer.

Gillian Lockitch, Anne C. Halstead, Susan Albersheim et al. · Clinical Chemistry · 1988 · 129 citations

Increased de novo Lipogenesis and Delayed Conversion of Large VLDL into Intermediate Density Lipoprotein Particles Contribute to Hyperlipidemia in Glycogen Storage Disease Type 1a

Robert Bandsma, Berthil H.C.M.T. Prinsen, Monique de Sain-van der Velden et al. · Pediatric Research · 2008 · 84 citations · Full text

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Decreased ketogenesis in von Gierke's disease (Type I glycogenosis)

Anna Binkiewicz, Boris Senior · The Journal of Pediatrics · 1973 · 33 citations

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