Neurology · 1988 · 182 citations · 0 references
MedicineNeurologyNeuroscienceEpilepsyEpileptologyMitochondrial GeneticsEpilepsy SyndromesMitochondrial DiseaseMitochondrial DisordersMitochondrial Neurological DisordersSeizure DisordersStatus EpilepticusEpileptic SyndromesLactate AcidosisLactic AcidosisMelas SyndromeMerrf SyndromeMitochondrial EncephalomyopathyMitochondrial SyndromesMyoclonic Epilepsy With Ragged Red Fibers
Severe prolonged migrainous symptoms and prolonged partial status epilepticus are characteristic features of the MELAS syndrome (mitochondrial encephalomyopathy, lactic acidosis, and stroke-like episodes). Maternal transmission previously found in myoclonus epilepsy and ragged-red fibers (MERRF), another mitochondrial disease, is suggested in this disorder as well.