The Korean Journal of Internal Medicine · 2001 · 13 citations · 9 references
MedicineOphthalmologyOcular DiseaseOcular ImmunologyOcular PathologyAutoimmune Eye DiseaseAutoimmune Ocular DiseaseAutoimmune VasculitisRetinal DiseaseRetinal Vascular DiseaseSystemic Lupus ErythematosusAnticardiolipin AntibodiesOcular VasculitisOphthalmologic FindingsOphthalmologic ManifestationsRetinal ArteriolesRetinal AutoantibodiesRetinal VasculopathySystemic Lupus Erythematosus Associations
Retinal vascular lesions are the most common ophthalmologic manifestation of systemic lupus erythematosus (SLE), occurring in 3% to 29% of cases, generally late in the disease. More rare is the severe vaso-occlusive disease, often termed "retinal vasculitis", which includes central retinal artery occlusion, multifocal arteriolar occlusions, extensive capillary nonperfusion and central venous occlusion. Patients with SLE and raised serum concentrations of anticardiolipin antibodies (ACA) have a higher risk of developing occlusive ocular vascular disease. We report a case in which retinal involvement was an earlier manifestation of SLE in a patient without ACA.
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Severe Retinal Vaso-Occlusive Disease in Systemic Lupus Erythematosus
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