Alveolar soft part sarcoma of the uterine corpus with pelvic lymph node metastasis: case report and literature review.

Abstract

Alveolar soft part sarcoma (ASPS) is a rare malignant soft tissue tumor, mainly localized in the extremities, occurring principally in adolescents and young adults. ASPS is uncommon in the female genital tract , and only 37 cases have been reported so far, including 9 cases in the uterine corpus and 17 cases in the uterine cervix. We here reported a case of ASPS occurring in the lower uterine segment . The case showed typical histological and immunohistochemical features. The patient had pelvic and para-aortic lymph node metastasis. To the best of our knowledge, it is the first such case described.