INTESTINAL POLYPOSIS AND ORAL PIGMENTATION: CASE REPORT

Abstract

Case Reports1 October 1956INTESTINAL POLYPOSIS AND ORAL PIGMENTATION: CASE REPORTROLAND W. RICHTERICH-VAN BAERLE, M.D., W. W. BYRNES, M.D., MARSHALL G. MORRIS, M.D., SAUL SCHEFF, M.D.ROLAND W. RICHTERICH-VAN BAERLE, M.D.Search for more papers by this author, W. W. BYRNES, M.D.Search for more papers by this author, MARSHALL G. MORRIS, M.D.Search for more papers by this author, SAUL SCHEFF, M.D.Search for more papers by this authorAuthor, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-45-4-707 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail Excerpt"A very remarkable case of familial polyposis of the mucous membranes, of the intestinal tract, and the nasopharynx accompanied by peculiar pigmentation of the skin, and the mucous membranes" is the title of an article by Peutz.1 The author described several members of a family with some or all of the manifestations of this unique syndrome. He felt that he was dealing with a new clinical entity of hereditary origin, and was able to demonstrate this syndrome in seven members of three generations of the same family, and to collect evidence that several others were probably afflicted.Only five more...Bibliography1. Peutz JL: Very remarkable case of familial polyposis of mucous membrane of intestinal tract and nasopharynx accompanied by peculiar pigmentation of skin and mucous membrane, Nederl. Maandschr. v. Geneesk. 10: 134, 1921. Google Scholar2. van DijkOudendal JAAJ: Adenoma of small intestine with a contribution to the knowledge of heredity in tumors, Nederl. tijdschr. v. Geneesk. 69: 966, 1925. Google Scholar3. Foster DB: Adenocarcinoma of small intestine in father and daughter, Brit. M. J. 2: 78, 1944. CrossrefMedlineGoogle Scholar4. TouraineCouder AF: Syndrome de Peutz (Lentiginopolypose digestive), Ann. de dermat. et syph. 5: 313, 1945. Google Scholar5. 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Surg. 141: 129, 1955. CrossrefMedlineGoogle Scholar23. ShermanTenner LFRJ: Melanin spots on the lips, oral mucosa, and digits associated with intestinal polyposis. Report of a case, Minnesota Med. 35: 1131, 1952. MedlineGoogle Scholar24. PoolGuice RMCE: Melanin spots: diagnostic significance in polyposis, Ann. Surg. 141: 664, 1955. CrossrefMedlineGoogle Scholar25. EversonAllen TCMJ: Subtotal colectomy with ileosigmoidostomy and fulguration of polyps in retained colon, Arch. Surg. 69: 806, 1954. CrossrefGoogle Scholar This content is PDF only. To continue reading please click on the PDF icon. Author, Article, and Disclosure InformationAffiliations: *Received for publication July 20, 1955.From the Departments of Medicine, Surgery and Roentgenology, Massachusetts Memorial Hospitals, Boston, Massachusetts.Requests for reprints should be addressed to R. W. Richterich-van Baerle, M.D., Boston University School of Medicine, 80 E. Concord St., Boston 18, Mass. PreviousarticleNextarticle Advertisement FiguresReferencesRelatedDetails Metrics Cited ByPolyposis of the small intestine, with pigmentation of the face, buccal mucosa, and digitsA case of peutz-jeghers syndromeGenetik der mit Pigmentstörungen einhergehenden DermatosenPeutz-Jeghers SyndromeThe oral tissues; the barometer of the bodyFamilial intestinal polyposis with melanosis oris: The syndrome of Peutz and JeghersTumors of the Gastrointestinal Tract and PancreasIntestinal polyposis with oral pigmentation 1 October 1956Volume 45, Issue 4Page: 707-717KeywordsAnemiaColonGastroenterology and hepatologyHospital medicineMucous membranesSurgery Issue Published: 1 October 1956 PDF DownloadLoading ...