Journal of Biological Chemistry · 1994 · 286 citations · 32 references
MedicineHematologyMolecular BiologyCytogeneticsMolecular OncologyOncogenesCancer CytogeneticsGene Fusions In CancerLymphoid NeoplasmsNeutrophil BiologyOncogene ActivationReceptor Tyrosine Kinase OncogenesBcr-abl1 Fusion GeneHematologic Malignancy FusionsKinase Fusion OncogenesLeukemia PathologyLeukemia-associated Fusion GenesOncogenic Fusion ProteinsPhosphotyrosine Binding Domain Adaptor ProteinsProtein Tyrosine Phosphorylation
The Philadelphia chromosome (Ph1), detected in virtually all cases of chronic myelogenous leukemia (CML), is formed by a reciprocal translocation between chromosome 9 and 22 that fuses Bcr-encoded sequences upstream of exon 2 of c-Abl. This oncogene produces a fusion protein, p210bcr-abl, in which the Abl tyrosine kinase activity is elevated. Using anti-phosphotyrosine immunoblotting, we have compared the pattern of phosphotyrosine-containing proteins from freshly prepared neutrophils of patients in the stable phase of CML to normal controls. The only consistent difference was the presence of a 39-kDa tyrosine-phosphorylated protein in 18 out of 18 neutrophil samples from CML patients that was not seen in normal controls. This same protein, as assessed by two-dimensional anti-phosphotyrosine immunoblotting, was also present in cell lines expressing p210bcr-abl, including K562 cells. Using K562 cells as a source of protein, the 39-kDa protein was purified and identified by microsequencing as Crkl, an SH2/SH3 adaptor protein related to the crk oncogene of the avian sarcoma virus, CT10. A direct interaction between Crkl and Abl has also been shown using a yeast two-hybrid screen.
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Human chronic myelogenous leukemia cell-line with positive Philadelphia chromosome
CB Lozzio, BB Lozzio · Blood · 1975 · 2.8K citations
Medicine, Hematology, Oncology +14