PubMed · 1987 · 74 citations · 0 references
Public HealthMaternal HealthObstetricsHigh-risk PregnancyMaternal MortalityObstetric ComplicationsMaternal ComplicationsMaternal Medical Complications In PregnancyMaternal Medical ConditionsMaternal MorbidityPregnancySevere Maternal MorbidityClassical Ehlers-danlos SyndromeConnective Tissue Disorder PathogenesisConnective Tissue Disorder SyndromesMaternal Death ClassificationObstetric Complications ManagementPregnancy MorbidityPregnancy-associated DeathsSevere Obstetric Complications
Ehlers-Danlos syndrome (EDS) is a rare connective tissue disorder known to be associated with complications during pregnancy. Recently, the syndrome has been subdivided into a number of types with different clinical manifestations. We report a maternal death with type IV, and review the literature for obstetric complications of the syndrome by type. A very high risk of maternal death with type IV is identified. Recommendations for managing pregnancies complicated by EDS are given.