Terry D. Butters

Novel oral treatment of Gaucher's disease with N-butyldeoxynojirimycin (OGT 918) to decrease substrate biosynthesis

Timothy M. Cox, Robin Lachmann, C. E. Hollak et al. · The Lancet · 2000 · 744 citations

Medicine, Pharmacology, Pharmacotherapy +4

N-butyldeoxynojirimycin is a novel inhibitor of glycolipid biosynthesis.

Frances M. Platt, Gabrielle R. Neises, Raymond A. Dwek et al. · Journal of Biological Chemistry · 1994 · 453 citations · Full text

Life Sciences, Biochemistry, Pharmacology +13

Infantile-onset symptomatic epilepsy syndrome caused by a homozygous loss-of-function mutation of GM3 synthase

Michael A. Simpson, Christos Proukakis, David A. Priestman et al. · Nature Genetics · 2004 · 385 citations

Life Sciences, Genetics, Molecular Genetics +16

Prevention of Lysosomal Storage in Tay-Sachs Mice Treated with <i>N</i> -Butyldeoxynojirimycin

Frances M. Platt, Gabrielle R. Neises, Gabriele Reinkensmeier et al. · Science · 1997 · 342 citations

Life Sciences, Biochemistry, Neuroscience +14

Imino sugars inhibit the formation and secretion of bovine viral diarrhea virus, a pestivirus model of hepatitis C virus: Implications for the development of broad spectrum anti-hepatitis virus agents

Nicole Zitzmann, Anand S. Mehta, Sandra Carrouée et al. · Proceedings of the National Academy of Sciences · 1999 · 326 citations

Life Sciences, Biochemistry, Molecular Biology +17