A Mouse Model of Mitochondrial Disease Reveals Germline Selection Against Severe mtDNA Mutations

Weiwei Fan, Katrina G. Waymire, Navneet Narula, +7

Science

BiologyMitochondrial MyopathyGenome InstabilityMitochondrial FunctionGenetic Disorder +11

Physiological diversity of mitochondrial oxidative phosphorylation

G. Benard, Benjamin Faustin, Emilie Passerieux, +7

American Journal of Physiology-Cell Physiology

Genomic landscape of human diversity across Madagascar

Denis Pierron, Margit Heiske, Harilanto Razafindrazaka, +33

Proceedings of the National Academy of Sciences

Tissue variation in the control of oxidative phosphorylation: implication for mitochondrial diseases

Rodrigue Rossignol, Thierry Letellier, Monique Malgat, +2

Biochemical Journal

Oxphos ControlMitochondrial Metabolic FluxesMitochondrial BiologyRedox BiologyOxidative Stress +19

Prevalence of rare mitochondrial DNA mutations in mitochondrial disorders

Sylvie Bannwarth, Vincent Procaccio, Anne Sophie Lebre, +33

Journal of Medical Genetics

Mitochondrial energetic and AKT status mediate metabolic effects and apoptosis of metformin in human leukemic cells

Sarah Scotland, Estelle Saland, Fabienne de Toni, +20

Leukemia

Mitochondrial FunctionBiochemistryMedicineApoptosisCell Death +6

Time course of differential mitochondrial energy metabolism adaptation to chronic hypoxia in right and left ventricles

Karine Nouette‐Gaulain, Monique Malgat, Christophe Rocher, +4

Cardiovascular Research

Functional dynamic compartmentalization of respiratory chain intermediate substrates: Implications for the control of energy production and mitochondrial diseases

G. Benard, Benjamin Faustin, Anne Galinier, +6

The International Journal of Biochemistry & Cell Biology

Energy MetabolismMitochondrial FunctionBiochemistryFunctional Dynamic CompartmentalizationMitochondrial Dynamic +10

Influence of mitochondrial DNA level on cellular energy metabolism: implications for mitochondrial diseases

Christophe Rocher, Jan‐Willem Taanman, Denis Pierron, +6

Journal of Bioenergetics and Biomembranes

Mitochondrial MyopathyCellular Energy MetabolismEnergy MetabolismMitochondrial DiseaseBiochemistry +12

Preservation of NADH ubiquinone-oxidoreductase activity by Src kinase-mediated phosphorylation of NDUFB10

Étienne Hébert-Chatelain, Caroline José, Nicolás Gutiérrez Cortés, +3

Biochimica et Biophysica Acta (BBA) - Bioenergetics

Reductive StressNadh Ubiquinone-oxidoreductase ActivitySrc Kinase-mediated PhosphorylationBiochemistryNatural Sciences +3